• A mutation in bovine keratin 5 causing epidermolysis bullosa simplex, transmitted by a mosaic sire 

      Ford, CA; Stanfield, AM; Spelman, RJ; Smits, B; Ankersmidt-Udy, AE; Cottier, K; Holloway, H; Walden, A; Al-Wahb, M; Bohm, E; Snell, RG; Sutherland, G
      Published 2005-01-01
      A mechanobullous skin disorder was identified in the progeny of a 3-y-old Friesian-Jersey crossbred bull. The condition presented as loss of skin and mucosa from contact areas and inflammation. Examination of skin samples ...
      Open Access
      Article
    • Do polymorphisms in the familial Parkinsonism genes contribute to risk for sporadic Parkinson's disease? 

      Sutherland, GT; Halliday, GM; Silburn, PA; Mastaglia, FL; Rowe, DB; Boyle, RS; O'Sullivan, JD; Ly, T; Wilton, SD; Mellick, GD
      Published 2009-01-01
      Recent whole genome association studies provided little evidence that polymorphisms at the familial Parkinsonism loci influence the risk for Parkinson's disease (PD). However, these studies are not designed to detect the ...
      Open Access
      Article
    • Haplotype analysis of the PARK 11 gene, GIGYF2, in sporadic Parkinson's disease 

      Sutherland, GT; Siebert, GA; Newman, JR; Silburn, PA; Boyle, RS; O'Sullivan, JD; Mellick, GD
      Published 2009-01-01
      Familial Parkinsonism (PARK) genes are strong candidates for conferring susceptibility to common forms of PD. However, most studies to date have provided little evidence that their common variants substantially influence ...
      Open Access
      Article
    • Disease-specific, neurosphere-derived cells as models for brain disorders 

      Matigian, N; Abrahamsen, G; Sutharsan, R; Cook, AL; Vitale, AM; Nouwens, A; Bellette, B; An, J; Anderson, M; Beckhouse, AG; Bennebroek, M; Cecil, R; Chalk, AM; Cochrane, J; Fan, Y; Féron, F; McCurdy, R; McGrath, JJ; Murrell, W; Perry, C; Raju, J; Ravishankar, S; Silburn, PA; Sutherland, GT; Mahler, S; Mellick, GD; Wood, SA; Sue, CM; Wells, CA; Mackay-Sim, A
      Published 2010-01-01
      There is a pressing need for patient-derived cell models of brain diseases that are relevant and robust enough to produce the large quantities of cells required for molecular and functional analyses. We describe here a new ...
      Open Access
      Article
    • Molecular investigation of TBP allele length: a SCA17 cellular model and population study 

      Reid, SJ; Rees, MI; van Room-Mom, WM; Jones, AL; MacDonald, ME; Sutherland, G; During, MJ; Faull, RL; Owen, MJ; Dragunow, M; Snell, RG
      Published 2003-01-01
      Recently, an inherited spinocerebellar ataxia (SCA17) has been attributed to polyglutamine coding expansions within the gene coding for human TATA-box binding protein (TBP). The normal repeat range is 25-42 units with ...
      Open Access
      Article